Myelodysplastic syndromes complicated by pancreatic iron overload: a case report and review of the literature
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摘要: 胰腺铁过载是一种罕见的疾病，以糖尿病首发，伴有胰腺形态学改变。临床上因缺乏对胰腺铁过载的认识和诊断标准，往往导致误诊，从而带来不必要的经济、身体和精神负担。本研究报告1例临床上被误诊为胰腺癌的骨髓增生异常综合征并发胰腺铁过载病例，旨在提高疾病认识和降低误诊率。Abstract: Pancreatic iron overload is a rare disease, presented with diabetes as the first symptom and with altered pancreatic morphology. Clinically, the lack of awareness and diagnostic criteria for pancreatic iron overload often leads to misdiagnosis of pancreatic disease, as well as unnecessary economic, physical, and mental burden. Here, we report a case of myelodysplastic syndromes complicated by pancreatic iron overload that was clinically misdiagnosed as pancreatic cancer, aiming at raising awareness and reducing the rate of misdiagnosis.
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Key words:
- pancreatic cancer /
- myelodysplastic syndromes /
- iron overload
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图 1 腹部增强CT图
A: 胰颈部局部密度欠均匀, 增强扫描动脉期胰颈部见团块状弱强化区, CT值约65 Hu; B: 门脉期及静脉期病灶呈轻度渐进性延迟强化.
Figure 1. The abdominal enhanced CT.
图 2 腹部增强MRI
A: 胰腺颈体似见约29 mm×24 mm稍长T1稍长T2信号影, 增强扫描呈渐进中度强化, 动态增强扫描动脉期低于正常胰腺实质强化; B：肝脏于T2WI像呈弥漫低信号, 同相位信号弥漫低于反相位.
Figure 2. The abdominal MRI.
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