MRI对Duchenne型肌营养不良患者大腿肌肉评估的研究进展

王奕乐; 闫锐

doi:10.12122/j.issn.1674-4500.2024.10.17

MRI对Duchenne型肌营养不良患者大腿肌肉评估的研究进展

doi: 10.12122/j.issn.1674-4500.2024.10.17

王奕乐^1,,
闫锐^{1, 2, ,}

1.
陕西中医药大学医学技术学院，陕西咸阳 712046
2.
西北妇女儿童医院医学影像中心，陕西西安 710061

基金项目:

陕西省科技厅重点研发计划 2024SF-YBXM-239

详细信息

作者简介:
王奕乐，在读硕士研究生，E-mail: wyl298064@163.com

通讯作者:
闫锐，博士，主任医师，E-mail: ruiyan01@sina.com

计量
- 文章访问数: 34
- HTML全文浏览量: 19
- PDF下载量: 1
- 被引次数: 0
出版历程
- 收稿日期: 2024-06-07
- 网络出版日期: 2024-11-02
- 刊出日期: 2024-10-20

Research progress of MRI assessment for thigh muscle in patients with Duchenne muscular dystrophy

WANG Yile^1
,,
YAN Rui^{1, 2
, ,}

1.
School of Medical Technology, Shaanxi University of Chinese Medicine, Xianyang 712046, China
2.
Medical Imaging Center, Northwest Women's and Children's Hospital, Xi'an 710061, China

摘要

摘要: Duchenne型肌营养不良（DMD）是一种高致残性及高致死性的遗传性神经肌肉疾病，其起病隐匿且进展较快，目前还没有治愈的方法。由于MRI可以无创性检测骨骼肌中病理改变并且量化疾病程度等优点，近年来，在神经肌肉疾病中的应用越来越广泛。本文针对常规MRI、定量MRI、多参数MRI以及MRI结合人工智能对监测Duchenne型肌营养不良患者的疾病程度进行综述，提出目前最新的研究进展及现阶段的局限性，并为后期展开相关研究，为疾病的诊断和精准量化病变肌肉的状态与监测肌肉病变的进展程度提供参考。
- Duchenne型肌营养不良 /
- 骨骼肌 /
- 磁共振成像 /
- 定量磁共振 /
- 深度学习
Abstract: Duchenne muscular dystrophy (DMD) is a highly disabling and lethal inherited neuromuscular disorder with insidious onset and fast-growing course, which currently has no cure. In recent years, MRI has become more and more widely used in neuromuscular diseases, due to the advantages of non-invasive detection of pathological changes in skeletal muscle and quantification of disorder course. This article reviews the latest research progress and the limitations at this stage of MRI, quantitive MRI, multimodel MRI and MRI combined with AI in monitoring the disease in patient with Duchenne muscular dystrophy, and in order to serve as a reference for the early diagnosis, quantitative evaluation and monitoring the progress of muscle lesions.
- Duchenne muscular dystrophy /
- skeletal muscle /
- MRI /
- quantitive MRI /
- deep learning

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参考文献(52)

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